Predominantly proximal motor variant of chronic inflammatory demyelinating polyradiculoneuropathy
https://doi.org/10.30629/2658-7947-2025-30-6-47-55
Abstract
The heterogeneity of the clinical and neurophysiological presentation of chronic inflammatory demyelinating polyradiculoneuropathy (CIDP), the wide spectrum of conditions mimicking CIDP, and the absence of specific biomarkers significantly complicate timely diagnosis. The article provides a detailed description of the clinical, neurophysiological, and neuroimaging features of predominantly proximal motor CIDP, as well as a review of the causes of initial misdiagnosis of a primary neuromuscular disease in the patient.
Keywords
chronic inflammatory demyelinating polyradiculoneuropathy,
CIDP,
atypical variant,
motor variant,
myopathy,
electroneuromyography,
plexus MRI,
differential diagnosis
Supporting agencies: The study had no sponsorship
About the Authors
D. A. Grishina
Russian Сenter of Neurology and Neurosciences
Russian Federation
Russian Federation
Moscow
N. A. Suponeva
Russian Сenter of Neurology and Neurosciences
Russian Federation
Russian Federation
Moscow
E. Yu. Fedotova
Russian Сenter of Neurology and Neurosciences
Russian Federation
Russian Federation
Moscow
E. P. Nuzhnyi
Russian Сenter of Neurology and Neurosciences
Russian Federation
Russian Federation
Moscow
S. N. Morozova
Russian Сenter of Neurology and Neurosciences
Russian Federation
Russian Federation
Moscow
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Review
For citations:
Grishina D.A., Suponeva N.A., Fedotova E.Yu., Nuzhnyi E.P., Morozova S.N. Predominantly proximal motor variant of chronic inflammatory demyelinating polyradiculoneuropathy. Russian neurological journal. 2025;30(6):47-55. (In Russ.) https://doi.org/10.30629/2658-7947-2025-30-6-47-55
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