Преимущественно проксимальный моторный вариант хронической воспалительной демиелинизирующей полирадикулоневропатии

   Гетерогенность клинической и нейрофизиологической картины при хронической воспалительной демиелинизирующей полирадикулоневропатии (ХВДП), широкий спектр ХВДП-подобных заболеваний, а также отсутствие биомаркеров значительно затрудняют своевременную диагностику болезни. В статье дается подробное описание особенностей клинической, нейрофизиологической и нейровизуализационной картины преимущественно проксимального моторного варианта ХВДП, проанализированы причины изначально ошибочной диагностики первично-мышечного заболевания у пациентки.

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