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Reccurent painful ophthalmoplegic neuropathy

https://doi.org/10.30629/2658-7947-2022-27-6-77-83

Abstract

Reccurent painful ophthalmoplegic neuropathy (the Tolosa–Hunt syndrome) occurs due to a nonspecific granulomatous infl ammation of the walls of the cavernous sinus and the intracavernous segment of the internal carotid artery. It consists of one or more oculomotor nerves dysfunction associated with peri- and retroorbital pain; spontaneous remissions and relapses are typical. Oculomotor nerve disorders may coincide with the onset of pain or follow it within a period of up to 2 weeks. Demonstration of granulomatosis in the walls of the cavernous sinus and the intracavernous segment of the internal carotid artery, superior orbital fissure or orbit by MRI or biopsy confi rms the diagnosis of Tolosa–Hunt syndrome (THS). Corticosteroid therapy leads to rapid (within 72 hours) pain relief and recovery of oculomotor nerve function. Here, we report a case of reccurent THS in 47-year-old men. Neuroimaging schowed a nonspecific inflammation in the superior orbital fissure-cavernous sinus region on left side and contrast-enhanced thickening dura mater.

About the Authors

M. Yu. Maksimova
Research Center of Neurology, Мinistry of Education and Science of Russia; A.I. Evdokimov Moscow State University of Medicine and Dentistry, Ministry of Health of Russia
Russian Federation

Moscow



S. N. Illarioshkin
Research Center of Neurology, Мinistry of Education and Science of Russia; A.I. Evdokimov Moscow State University of Medicine and Dentistry, Ministry of Health of Russia
Russian Federation

Moscow



I. A. Savizkaya
Research Center of Neurology, Мinistry of Education and Science of Russia
Russian Federation

Moscow



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Review

For citations:


Maksimova M.Yu., Illarioshkin S.N., Savizkaya I.A. Reccurent painful ophthalmoplegic neuropathy. Russian neurological journal. 2022;27(6):77-83. (In Russ.) https://doi.org/10.30629/2658-7947-2022-27-6-77-83

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